Clicking on any metabolite link will take you to the Human Metabolome Database.
Displaying diseases 57 - 60 of 277 in total
Maple syrup urine disease  (248600 )
MetaboliteConcentration in UrinePatient StatusAgeSexReferenceDetails
3-Methyl-2-oxovaleric acid (HMDB0000491) 209.0 +/- 35.0 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
L-Arginine (HMDB0000517) 50.3 +/- 10.6 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Citric acid (HMDB0000094) 576.1 +/- 15.2 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Creatinine (HMDB0000562) 14416 +/- 983 uMAbnormalAdult (>18 years old)Both details
Ethanolamine (HMDB0000149) 99.7 +/- 3.3 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Glycine (HMDB0000123) 233.7 +/- 10.5 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Histidine (HMDB0000177) 171.8 +/- 4.3 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Taurine (HMDB0000251) 98.3 +/- 7.1 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Trimethylamine N-oxide (HMDB0000925) 33.1 +/- 1.9 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
alpha-Ketoisovaleric acid (HMDB0000019) 550.00 (300.00-800.00) umol/mmol creatinineAbnormalAdult (>18 years old)Both
  • MetaGene: Metabol...
details
1-Methylhistidine (HMDB0000001) 31 +/- 11 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Acetic acid (HMDB0000042) 13.2 +/- 5.5 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Betaine (HMDB0000043) 14.2 +/- 0.9 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Glutamine (HMDB0000641) 52.8 +/- 26.3 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Hippuric acid (HMDB0000714) 234.1 +/- 15.3 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
3-Hydroxy-4,5-dimethyl-2(5H)-furanone (HMDB0031306) Not QuantifiedAbnormalAdult (>18 years old)Not Specified details
alpha-Ketoisovaleric acid (HMDB0000019) 550.00 (300.00-800.00) umol/mmol creatinineAbnormalChildren (1-13 years old)Both
  • MetaGene: Metabol...
details
2-Hydroxy-3-methylpentanoic acid (HMDB0000317) Not QuantifiedAbnormalNot AvailableNot Available details
Hydroxyisocaproic acid (HMDB0000746) 41.5 (3.00-80.00) umol/mmol creatinineAbnormalChildren (1-13 years old)Both
  • MetaGene: Metabol...
details
Cystathioninuria  (219500 )
MetaboliteConcentration in UrinePatient StatusAgeSexReferenceDetails
L-Cystathionine (HMDB0000099) 381.0 +/- 29.0 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
L-Cystathionine (HMDB0000099) 5.3 (1.0-9.6) umol/mmol creatinineAbnormalAdult (>18 years old)Both
  • MetaGene: Metabol...
details
L-Cystathionine (HMDB0000099) 6.139 umol/mmol creatinineAbnormalChildren (1-13 years old)Female details
L-Cystathionine (HMDB0000099) 6.897 umol/mmol creatinineAbnormalChildren (1-13 years old)Female details
L-Cystathionine (HMDB0000099) 182.14 umol/mmol creatinineAbnormalChildren (1-13 years old)Female details
L-Cystathionine (HMDB0000099) 84.795 umol/mmol creatinineAbnormalChildren (1-13 years old)Female details
L-Cystathionine (HMDB0000099) 216.623 umol/mmol creatinineAbnormalChildren (1-13 years old)Female details
L-Cystathionine (HMDB0000099) 1001.0 (158.0-1843.8) umol/mmol creatinineAbnormalChildren (1-13 years old)Both
  • MetaGene: Metabol...
details
N-Acetylcystathionine (HMDB0002381) 20.0 (8.8-31.0) umol/mmol creatinineAbnormalChildren (1-13 years old)Both
  • MetaGene: Metabol...
details
Prostate cancer  (176807 )
MetaboliteConcentration in UrinePatient StatusAgeSexReferenceDetails
L-Sorbose (HMDB0001266) 0.5 (0.0-1.0) umol/mmol creatinineAbnormalAdult (>18 years old)Both details
N-Formyl-L-methionine (HMDB0001015) 0.5 (0.0-1.0) umol/mmol creatinineAbnormalAdult (>18 years old)Both details
N-Acetyl-L-glutamic acid (HMDB0001138) 0.5 (0.0-1.0) umol/mmol creatinineAbnormalAdult (>18 years old)Both details
N-Acetyl-L-alanine (HMDB0000766) 0.5 (0.0-1.0) umol/mmol creatinineAbnormalAdult (>18 years old)Both details
L-Allothreonine (HMDB0004041) 0.5 (0.0-1.0) umol/mmol creatinineAbnormalAdult (>18 years old)Both details
6-Hydroxynicotinic acid (HMDB0002658) 0.5 (0.0-1.0) umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Methyldopa (HMDB0011754) 0.5 (0.0-1.0) umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Androstanediol (HMDB0000495) 0.10 +/- 0.04 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Sarcosine (HMDB0000271) Not QuantifiedAbnormalAdult (>18 years old)Male details
Shikimic acid (HMDB0003070) Not QuantifiedAbnormalAdult (>18 years old)Both details
Spina Bifida  (182940 )
MetaboliteConcentration in UrinePatient StatusAgeSexReferenceDetails
p-Hydroxyphenylacetic acid (HMDB0000020) 25.0 (7.0-50.5) umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Displaying diseases 57 - 60 of 277 in total