- Metabolite
- HMDB0031306 (3-Hydroxy-4,5-dimethyl-2(5H)-furanone)
- Biospecimen
- Urine
- Status
- Detected but not Quantified
- Data source
- Referenced
- Concentration
- Not Quantified
- Age
- Adult (>18 years old)
- Sex
- Not Specified
- Condition
- Maple syrup urine disease
References
- Podebrad F, Heil M, Reichert S, Mosandl A, Sewell AC, Bohles H: 4,5-dimethyl-3-hydroxy-2[5H]-furanone (sotolone)--the odour of maple syrup urine disease. J Inherit Metab Dis. 1999 Apr;22(2):107-14. [PubMed:10234605 ]