Clicking on any metabolite link will take you to the Human Metabolome Database.
Displaying diseases 161 - 164 of 277 in total
Sulfite oxidase deficiency, ISOLATED  (272300 )
MetaboliteConcentration in UrinePatient StatusAgeSexReferenceDetails
Cysteine-S-sulfate (HMDB0000731) 25 (10 - 40) uMAbnormalChildren (1-13 years old)Not Specified details
L-Cysteine (HMDB0000574) <5 uMAbnormalInfant (0-1 year old)Male
  • Clinical and Labo...
details
Homocysteine (HMDB0000742) <0.700 uMAbnormalInfant (0-1 year old)Male
  • Clinical and Labo...
details
L-Cysteine (HMDB0000574) 5000000 uMAbnormalChildren (1-13 years old)Female details
Ammonia (HMDB0000051) 49 uMAbnormalInfant (0-1 year old)Male
  • Clinical and Labo...
details
Lactic acid (HMDB0000190) 1600 uMAbnormalInfant (0-1 year old)Male
  • Clinical and Labo...
details
Taurine (HMDB0000251) 188 uMAbnormalInfant (0-1 year old)Male
  • Clinical and Labo...
details
Uric acid (HMDB0000289) 244 uMAbnormalInfant (0-1 year old)Male
  • Clinical and Labo...
details
Uric acid (HMDB0000289) 148.712-190.351 uMAbnormalInfant (0-1 year old)Both details
Cysteine-S-sulfate (HMDB0000731) 14000000 uMAbnormalChildren (1-13 years old)Female details
Fumarase deficiency  (606812 )
MetaboliteConcentration in UrinePatient StatusAgeSexReferenceDetails
Ammonia (HMDB0000051) 139 - 299 uMAbnormalInfant (0-1 year old)Male details
L-Tyrosine (HMDB0000158) 257 uMAbnormalInfant (0-1 year old)Male details
L-Threonine (HMDB0000167) 313 uMAbnormalInfant (0-1 year old)Male details
L-Asparagine (HMDB0000168) 99 uMAbnormalInfant (0-1 year old)Male details
Histidine (HMDB0000177) 130 uMAbnormalInfant (0-1 year old)Male details
Lysine (HMDB0000182) 107 uMAbnormalInfant (0-1 year old)Male details
Serine (HMDB0000187) 263 uMAbnormalInfant (0-1 year old)Male details
Ornithine (HMDB0000214) 77 uMAbnormalInfant (0-1 year old)Male details
Glutamine (HMDB0000641) 430 uMAbnormalInfant (0-1 year old)Male details
Leucine (HMDB0000687) 66 uMAbnormalInfant (0-1 year old)Male details
Methionine (HMDB0000696) 70 uMAbnormalInfant (0-1 year old)Male details
Citrulline (HMDB0000904) 181 uMAbnormalInfant (0-1 year old)Male details
Primary hypomagnesemia  (248250 )
MetaboliteConcentration in UrinePatient StatusAgeSexReferenceDetails
D-Glucose (HMDB0000122) 4995.673-5106.688 uMAbnormalAdult (>18 years old)Male details
Urea (HMDB0000294) 1998.16-2497.70 uMAbnormalAdult (>18 years old)Male details
Calcium (HMDB0000464) 1472.129 uMAbnormalChildren (1-13 years old)Male details
Calcium (HMDB0000464) 1534.508 uMAbnormalChildren (1-13 years old)Male details
Calcium (HMDB0000464) 1580 +/- 330 uMAbnormalChildren (1-13 years old)Both details
Calcium (HMDB0000464) 798.443-1047.956 uMAbnormalAdult (>18 years old)Male details
Magnesium (HMDB0000547) 123.431 uMAbnormalAdult (>18 years old)Male details
Magnesium (HMDB0000547) 240 +/- 110 uMAbnormalChildren (1-13 years old)Both details
Magnesium (HMDB0000547) 320-610 uMAbnormalChildren (1-13 years old)Both details
Bilirubin (HMDB0000054) 6.842-20.525 uMAbnormalAdult (>18 years old)Male details
Cholesterol (HMDB0000067) 4629.468 uMAbnormalAdult (>18 years old)Male details
Uric acid (HMDB0000289) 231.991-243.887 uMAbnormalAdult (>18 years old)Male details
Calcium (HMDB0000464) 2395.329-2869.405 uMAbnormalAdult (>18 years old)Male details
Chloride ion (HMDB0000492) 96000-100000 uMAbnormalAdult (>18 years old)Male details
Creatinine (HMDB0000562) 53.042 uMAbnormalAdult (>18 years old)Male details
Creatinine (HMDB0000562) 45-104 uMAbnormalChildren (1-13 years old)Both details
Potassium (HMDB0000586) 3700-4300 uMAbnormalAdult (>18 years old)Male details
Sodium (HMDB0000588) 138000-139000 uMAbnormalAdult (>18 years old)Male details
alpha-D-Glucose (HMDB0003345) 4995.673-5106.688 uMAbnormalAdult (>18 years old)Male details
Primary hyperoxaluria I
MetaboliteConcentration in UrinePatient StatusAgeSexReferenceDetails
Oxalic acid (HMDB0002329) 37.310-243.200 uMAbnormalChildren (1-13 years old)Both details
Displaying diseases 161 - 164 of 277 in total