Clicking on any metabolite link will take you to the Human Metabolome Database.
Displaying diseases 165 - 168 of 277 in total
Hyperdibasic aminoaciduria I  (222690 )
MetaboliteConcentration in UrinePatient StatusAgeSexReferenceDetails
Lysine (HMDB0000182) 111.677-220.880 umol/mmol creatinineAbnormalChildren (1 - 13 years old)Female details
L-Cystine (HMDB0000192) 6.681-2.305 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Ornithine (HMDB0000214) 8.897-14.0297 umol/mmol creatinineAbnormalChildren (1 - 13 years old)Female details
L-Arginine (HMDB0000517) 3.635-9.216 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Lysine (HMDB0000182) 41.840-220.880 umol/mmol creatinineAbnormalChildren (1-13 years old)Female details
Lysine (HMDB0000182) 30.704-356.533 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
L-Cystine (HMDB0000192) 4.423-24.136 umol/mmol creatinineAbnormalChildren (1-13 years old)Female details
L-Cystine (HMDB0000192) 6.681-21.125 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Ornithine (HMDB0000214) 4.363-53.381 umol/mmol creatinineAbnormalChildren (1-13 years old)Female details
Ornithine (HMDB0000214) 4.106-35.759 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
L-Arginine (HMDB0000517) 2.985-10.644 umol/mmol creatinineAbnormalChildren (1-13 years old)Female details
L-Arginine (HMDB0000517) 3.635-11.747 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Lysine (HMDB0000182) 30.704-137.431 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
L-Cystine (HMDB0000192) 5.975-24.136 umol/mmol creatinineAbnormalChildren (1 - 13 years old)Female details
Ornithine (HMDB0000214) 4.106-13.859 umol/mmol creatinineAbnormalAdult (>18 years old)Both details
L-Arginine (HMDB0000517) 6.490-10.644 umol/mmol creatinineAbnormalChildren (1 - 13 years old)Female details
2-Aminoadipic aciduria  (204750 )
MetaboliteConcentration in UrinePatient StatusAgeSexReferenceDetails
Oxoadipic acid (HMDB0000225) 520-970 umol/mmol creatinineAbnormalChildren (1-13 years old)Female details
Aspartylglucosaminuria  (208400 )
MetaboliteConcentration in UrinePatient StatusAgeSexReferenceDetails
Aspartylglycosamine (HMDB0000489) 0.6 (0.20-1.00) umol/mmol creatinineAbnormalAdult (>18 years old)Both
  • MetaGene: Metabol...
details
Aspartylglycosamine (HMDB0000489) 175.0 (100.0-250.0) umol/mmol creatinineAbnormalChildren (1-13 years old)Both
  • MetaGene: Metabol...
details
Aspartylglycosamine (HMDB0000489) 87.680 (39.963-166.0153) umol/mmol creatinineAbnormalAdult (>18 years old)Both details
Aspartylglycosamine (HMDB0000489) 70.383 (30.420-97.621) umol/mmol creatinineAbnormalChildren (1-13 years old)Both details
Xanthinuria type 1  (278300 )
MetaboliteConcentration in UrinePatient StatusAgeSexReferenceDetails
Hypoxanthine (HMDB0000157) 65 umol/mmol creatinineAbnormalAdult (>18 years old)Male details
Hypoxanthine (HMDB0000157) 61.8-138.0 umol/mmol creatinineAbnormalChildren (1-13 years old)Both details
Uric acid (HMDB0000289) 1.19 umol/mmol creatinineAbnormalChildren (1-13 years old)Male details
Uric acid (HMDB0000289) 1.983 umol/mmol creatinineAbnormalAdult (>18 years old)Female details
Uric acid (HMDB0000289) 10 umol/mmol creatinineAbnormalAdult (>18 years old)Male details
Uric acid (HMDB0000289) 0-47 umol/mmol creatinineAbnormalChildren (1-13 years old)Both details
Xanthine (HMDB0000292) 146.978 umol/mmol creatinineAbnormalAdult (>18 years old)Female details
Xanthine (HMDB0000292) 192.202 umol/mmol creatinineAbnormalChildren (1-13 years old)Male details
Xanthine (HMDB0000292) 193 umol/mmol creatinineAbnormalAdult (>18 years old)Male details
Xanthine (HMDB0000292) 164.5-349.3 umol/mmol creatinineAbnormalChildren (1-13 years old)Both details
Displaying diseases 165 - 168 of 277 in total