Concentration Details

Metabolite
HMDB0000317 (2-Hydroxy-3-methylpentanoic acid)
Biospecimen
Urine
Status
Detected but not Quantified
Data source
Referenced
Concentration
Not Quantified
Age
Not Available
Sex
Not Available
Condition
Dihydrolipoyl DH (E3) deficiency
References
    1. Kumps A, Duez P, Mardens Y: Metabolic, nutritional, iatrogenic, and artifactual sources of urinary organic acids: a comprehensive table. Clin Chem. 2002 May;48(5):708-17. [PubMed:11978597 ]