Concentration Details

Metabolite
HMDB0000355 (3-Hydroxymethylglutaric acid)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
137.4 umol/mmol creatinine
Age
Infant (0-1 year old)
Sex
Not Specified
Condition
Metabolic acidosis
References
    1. Wysocki SJ, Wilkinson SP, Hahnel R, Wong CY, Panegyres PK: 3-Hydroxy-3-methylglutaric aciduria, combined with 3-methylglutaconic aciduria. Clin Chim Acta. 1976 Aug 2;70(3):399-406. [PubMed:947633 ]