Concentration Details

Metabolite
HMDB0001844 (Methylsuccinic acid)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
1.9 (1.3-2.5) umol/mmol creatinine
Age
Adult (>18 years old)
Sex
Both
Condition
Refsum's disease
References
    1. Greter J, Lindstedt S, Steen G: 2,6-Dimethyloctanedioic acid--a metabolite of phytanic acid in Refsum's disease. Clin Chem. 1983 Mar;29(3):434-7. [PubMed:6186413 ]