Concentration Details

Metabolite
HMDB0000459 (3-Methylcrotonylglycine)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
225.0 (0.00-450.0) umol/mmol creatinine
Age
Children (1-13 years old)
Sex
Both
Condition
3-Hydroxy-3-Methylglutaryl-CoA Lyase Deficiency
References
    1. G.Frauendienst-Egger, Friedrich K. Trefz (2017). MetaGene: Metabolic & Genetic Information Center (MIC: http://www.metagene.de). METAGENE consortium.