Concentration Details

Metabolite
HMDB0000208 (Oxoglutaric acid)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
1119.294 umol/mmol creatinine
Age
Infant (0-1 year old)
Sex
Male
Condition
Dihydrolipoamide Dehydrogenase Deficiency
References
    1. Kuhara T, Shinka T, Inoue Y, Matsumoto M, Yoshino M, Sakaguchi Y, Matsumoto I: Studies of urinary organic acid profiles of a patient with dihydrolipoyl dehydrogenase deficiency. Clin Chim Acta. 1983 Sep 30;133(2):133-40. [PubMed:6688766 ]