Concentration Details

Metabolite
HMDB0006535 (beta-1,4-Mannosyl-N-acetylglucosamine)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
169.559-190.427 umol/mmol creatinine
Age
Not Specified
Sex
Not Specified
Condition
beta-Mannosidosis
References
    1. Tjoa S, Wenger DA, Fennessey PV: Quantitative analysis of disaccharides in the urine of beta-mannosidosis patients. J Inherit Metab Dis. 1990;13(2):187-94. [PubMed:2116550 ]