Concentration Details

Metabolite
HMDB0000245 (Porphobilinogen)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
9.7 (21.8-10.5) umol/mmol creatinine
Age
Adult (>18 years old)
Sex
Both
Condition
Acute intermittent porphyria
Comments
Median (min.-max.). 72 months post-acute attack
References
    1. Marsden JT, Rees DC: Urinary excretion of porphyrins, porphobilinogen and delta-aminolaevulinic acid following an attack of acute intermittent porphyria. J Clin Pathol. 2014 Jan;67(1):60-5. doi: 10.1136/jclinpath-2012-201367. Epub 2013 Aug 1. [PubMed:23908454 ]