Concentration Details

Metabolite
HMDB0000182 (Lysine)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
3.414 umol/mmol creatinine
Age
Children (1-13 years old)
Sex
Male
Condition
Alpha-aminoadipic and alpha-ketoadipic aciduria
Comments
n=1
References
    1. Takechi T, Okada T, Wakiguchi H, Morita H, Kurashige T, Sugahara K, Kodama H: Identification of N-acetyl-alpha-aminoadipic acid in the urine of a patient with alpha-aminoadipic and alpha-ketoadipic aciduria. J Inherit Metab Dis. 1993;16(1):119-26. [PubMed:8487492 ]