Concentration Details

Metabolite
HMDB0000678 (Isovalerylglycine)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
4474.586 umol/mmol creatinine
Age
Children (1 - 13 years old)
Sex
Female
Condition
Isovaleric acidemia
References
    1. Krieger I, Tanaka K: Therapeutic effects of glycine in isovaleric acidemia. Pediatr Res. 1976 Jan;10(1):25-9. [PubMed:1246461 ]