Concentration Details

Metabolite
HMDB0000603 (cis-4-Decenedioic acid)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
787.681 umol/mmol creatinine
Age
Children (1 - 13 years old)
Sex
Not Specified
Condition
Medium Chain Acyl-CoA Dehydrogenase Deficiency
Comments
22 h fasting
References
    1. Tserng KY, Jin SJ, Kerr DS, Hoppel CL: Abnormal urinary excretion of unsaturated dicarboxylic acids in patients with medium-chain acyl-CoA dehydrogenase deficiency. J Lipid Res. 1990 May;31(5):763-71. [PubMed:2380628 ]