Concentration Details

Metabolite
HMDB0000350 (3-Hydroxysebacic acid)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
10.628-308.767 umol/mmol creatinine
Age
Children (1-13 years old)
Sex
Not Specified
Condition
Medium Chain Acyl-CoA Dehydrogenase Deficiency
References
    1. Duran M, De Klerk JB, Wadman SK, Bruinvis L, Ketting D: The differential diagnosis of dicarboxylic aciduria. J Inherit Metab Dis. 1984;7 Suppl 1:48-51. [PubMed:6434845 ]