Concentration Details

Metabolite
HMDB0000354 (2-Methyl-3-hydroxybutyric acid)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
370.837-809.510 umol/mmol creatinine
Age
Children (1 - 13 years old)
Sex
Female
Condition
Ketosis
Comments
Ketosis in 3-Ketothiolase deficiency
References
    1. B. Middleton et al. (1986). B. Middleton et al. 3-Ketothiolase deficiency. Eur J Pediatr (1986) 144:586-589. Eur J Pediatr.