- Metabolite
- HMDB0000678 (Isovalerylglycine)
- Biospecimen
- Urine
- Status
- Detected and Quantified
- Data source
- Referenced
- Concentration
- 15-195 umol/mmol creatinine
- Age
- Adolescent (13-18 years old)
- Sex
- Male
- Condition
- Isovaleric acidemia
References
- Yasutsugu Chinen, Sadao Nakamura, Kunihito Tamashiro, Osamu Sakamoto, Kyoko Tashiro, Takahiro Inokuchi, Koichi Nakanishi (2017). Isovaleric acidemia: Therapeutic response to supplementation with glycine, /react-text l react-text: 82 -carnitine, or both in combination and a 10-year. follow-up case study. Molecular Genetics and Metabolism Reports. Volume 11, June 2017, Pages 2-5. Molecular Genetics and Metabolism Reports.