Concentration Details

Metabolite
HMDB0000678 (Isovalerylglycine)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
15-195 umol/mmol creatinine
Age
Adolescent (13-18 years old)
Sex
Male
Condition
Isovaleric acidemia
References
    1. Yasutsugu Chinen, Sadao Nakamura, Kunihito Tamashiro, Osamu Sakamoto, Kyoko Tashiro, Takahiro Inokuchi, Koichi Nakanishi (2017). Isovaleric acidemia: Therapeutic response to supplementation with glycine, /react-text l react-text: 82 -carnitine, or both in combination and a 10-year. follow-up case study. Molecular Genetics and Metabolism Reports. Volume 11, June 2017, Pages 2-5. Molecular Genetics and Metabolism Reports.